Elastosis perforans serpiginosa eps is a rare chronic perforating dermatosis which was first described in 1953 by lutz. Disorders of transepidermal elimination, international. Dermis elastosis perforante serpiginosa information on. Elastosis perforans serpiginosa eps is a rare condition within the group of perforating dermatoses.
Benign prostatic hyperplasia with lower urinary tract symptoms. Eps, colagenosis perforante re activa, foliculitis perforante. Since it was first described by lutz in 1953, eps is. Elastosis perforans serpiginosa disease definition a rare acquired dermis elastic tissue disorder with increased elastic tissue characterized by focal dermal elastosis and transepidermal elimination of abnormal elastic fibers, presenting as small keratotic papules or plaques arranged in groups in serpiginous or annular patterns on the neck. Elastosis perforans serpiginosa definition of elastosis. The list of acronyms and abbreviations related to eps elastosis perforans serpiginosa. If you would like a large, unwatermarked image for your web page or blog, please purchase the appropriate license. Actinic elastosis, also known as solar elastosis, is an accumulation of abnormal elastin elastic tissue in the dermis of the skin, or in the conjunctiva of the eye, which occurs as a result of the cumulative effects of prolonged and excessive sun exposure, a process known as photoaging. Retrogressive change in cutaneous connective tissue resulting in excessive amounts of material which give the. Elastosis perforans serpiginosum accessed 27 august 2018. Anatomia inimii pdf a summary of the 5 cases of elastosis perforance serpiginosa reported in sfrpiginosa korean literature including our case. In idiopathic elastosis perforans serpiginosa, the cause and risk factors for the condition remain unknown. Elastosis perforans serpiginosa with a history of familial involvement.
In 1952 lutz 1 described a peculiar serpiginous keratotie eruption that was present on the sides of the neck of a 21yearold man for 8 years. It is characterized by the synthesis of anomalous elastic fibres that are eliminated through perf. Elastosis perforans serpiginosa eps represents a distinct entity within the spectrum of perforating dermatoses. You may not embed one of our images on your web page without a link back to our site. Eps is characterized by the presence of multiple tiny papules on the neck or face in a winding pattern. Summary elastosis perforans serpiginosa is a rare chronic dermatosis characterized by extrusion of altered elastic fibers through the e pidermis. Elastosis perforans serpiginosa in association with scabies mite. Elastosis perforans serpiginosa has also been thought to be resultant of an injured epidermal barrier. Elastosis perforans serpiginosa, therapeutics introduction elastosis perforans serpiginosa eps is a rare skin condition characterized by hyperkeratotic papules, transepidermal elimination of abnormal elastic fibers, and focal dermal elastosis. Feb 17, 2014 elastosis perforans serpiginosa is a rare skin disease characterized by transepidermal elimination of abnormal elastic fibers. Always seek professional medical advice about any treatment or change in treatment. We present the case of a patient with down syndrome and hyperkeratotic papules located on the superior and. Elastosis perforans serpiginosa is triggered by excess production of.
Dermis elastosis perforante serpiginosa information on the. Disorders of transepidermal elimination disorders of transepidermal elimination woo, thomas y rasmussen, james e. Elastosis perforans serpiginosa may be distinguished morphologically and histologically from oth. Elastotic definition of elastotic by medical dictionary. Pathology outlines elastosis perforans serpiginosum. Brightly eosinophilic fibres are seen within the extruded material, mixed with. It is also dependent upon the underlying health condition, if any, associated with it. Elastosis perforans serpiginosa is one of four classic primary perforating disorders along with reactive perforating collagenosis, perforating folliculitis, and kyrle disease. Elastosis perforans serpiginosa is an infrequent skin dermatosis of unknown.
It is a rare disorder characterized by transepidermal elimination of altered elastic fibers. Transepidermal elimination te is a mechanism whereby foreign or altered constituents can be removed from the dermis. Elastosis perforans serpiginosaelastosis perforans. Dermis solar or senile elastosis information on the. If you would like a large, unwatermarked image for your web page or. Eps present as asymptomatic to pruritic groups of keratotic papules coalescing in a arcuate serpiginous distribution. Elastosis perforans serpiginosa is considered as mild dermatosis, which is not accompanied by involvement of other organs 2. Enfermedades adquiridas del tejido elastico sciencedirect. Outcomesresolutions the prognosis of elastosis perforans serpiginosa depends upon the severity of the condition. Localized idiopathic elastosis perforans serpiginosa effectively treated by the coherent ultrapulse 5000c aesthetic laser. Nodular elastosis definition of nodular elastosis by the. Elastosis perforans serpiginosa eps is a rare reactive perforating dermatosis that is characterized by the transepidermal elimination of abnormal elastic fibers. Cutaneous and ocular manifestations of down syndrome.
The cause of abnormal elastic tissue is unknown but may be from a genetic mutation or external factors such as penicillamine. A compromised epidermal barrier or a dermal response to chronic trauma may contribute to the development of eps. Diagnosis is based on clinical and histopathologic aspects. The code is valid for the year 2020 for the submission of hipaacovered transactions. Dpenicillamine induced elastosis perforans serpiginosa mimicking acne keloidalis nuchae. Solar or senile elastosis, elastosis senilis, actinic elastosis. He named the lesion keratosis follieularis serpiginosa. Abnormal skin fibre tissue forms from the inner skin layer to the outer skin layer which in turn causes the top skin layer to respond to it as if it were a foreign particle i. Elastosis cutanea envejecimiento prematuro y estrias by. In both cases, the pathological study of the lesions disclosed a reactive perforating. Elastosis perforans serpiginosa symptoms, diagnosis. Differential diagnosis shall include 1 favreracouchot syndrome nodular elastosis with cysts and comedones that tends to affect bilateral forehead and cheeks due to solar damage.
Elastosis perforans serpiginosa is a rare primary perforating disorder. Idiopathic elastosis perforans serpiginosa dovemed. Elastosis perforans serpiginosa synonyms elastoma intrapapillare perforans verruciforme keratosis follicularis serpiginosa serpiginous perforating elastosis perforating elastoma elastoma intrapapillare perforans presentation stereotypical age and sex most common during the second decade of life and in males mostly distribution of lesions symmetric, neck and upper extremities chiefly, but face. Low power of histology of elastosis perforans serpiginosa demonstrates a column of keratotic debris forming a focal invagination through a hyperplastic epidermis figure 1. Elastosis perforans serpiginosa is a rare skin disease characterized by transepidermal elimination of abnormal elastic fibers. Jan 01, 2020 a rare acquired dermis elastic tissue disorder with increased elastic tissue characterized by focal dermal elastosis and transepidermal elimination of abnormal elastic fibers, presenting as small keratotic papules or plaques arranged in groups in serpiginous or annular patterns on the neck, face, and arms, while other areas are less frequently affected. Elastosis definition of elastosis by the free dictionary. Sorry, we are unable to provide the full text but you may find it at the following locations. Treatment has included various modalities and cryotherapy is one of the effective options.
This sagging skin is defined significantly by the condition of the underlying muscles. Elasticvan gieson evg staining highlights elastic fibres, so in this condition will show black fibres transgressing through the focus of transepidermal elimination figures 5, 6. This process involves unique morphologic alterations of the epidermis, which forms a. Elastosis perforans serpiginosa eps is a rare skin disease in which abnormal elastic tissue fibers, other connective tissue elements, and cellular debris are expelled from the papillary dermis through the epidermis transepithelial elimination. Pdf elastosis perforans serpiginosa a rare case report. Apr 29, 2016 elastosis perforans serpiginosa is an uncommon and chronic dermatosis characterized by transepidermal elimination of abnormal elastic fibers originating in the dermis.
Elastosis perforans serpiginosa in association with. In 1955 miescher further characterized this entity on the pathological findings. Skin elasticity is what determines the skins ability to stretch and then return to its normal state. Elastosis perforans serpiginosa occurs because the epidermis the outer layer of the skin perceives abnormal elastic tissue to be a foreign object, thus responding through an inflammatory attack. Always seek professional medical advice about any treatment or change in treatment plans. Elastosis perforans serpiginosa is a rare chronic dermatosis characterized by extrusion of altered elastic fibers through the epidermis. Mar 06, 2019 elastosis perforans serpiginosa eps is a rare skin disease in which abnormal elastic tissue fibers, other connective tissue elements, and cellular debris are expelled from the papillary dermis through the epidermis transepithelial elimination. The list of treatments mentioned in various sources for elastosis perforans serpiginosa includes the following list. A rare skin condition characterized by the development of small, usually red, bumps on the skin. Closer inspection identifies material undergoing transepidermal elimination figure 2. This condition classically presents as small papules arranged in serpiginous or annular patterns on the neck, face, arms, or other flexural areas. Pdf elastosis perforans serpiginosa is a rare skin disease characterized by transepidermal elimination of abnormal elastic fibers. Eps is characterized by the presence of multiple tiny. Elastosis perforans serpiginosa eps is a rare skin disorder in which abnormal elastic tissue fibre passes from the papillary dermis inner layer of skin to the epidermis outer layer of skin, described as transepithelial elimination.
Nodular elastosis article about nodular elastosis by the. A loss of elasticity tone and firmness in the skin, known as elastosis, is a natural part of the aging process for most people. Elastosis perforans serpiginosa eps is a chronic and infrequent dermatosis, belonging to the group of primary perforating dermatoses. Sep 05, 2018 what is the prognosis of elastosis perforans serpiginosa. Dpenicillamine induced elastosis perforans serpiginosa mimicking acne. Elastosis perforans serpiginosa is a unique perforating disorder characterized by transepidermal elimination of elastic fibers and distinctive clinical lesions, which are serpiginous in distribution and can be associated with specific diseases. Elastosis perforans serpiginosa article about elastosis. Report of a family with a chromosomal investigation. Treatment list for elastosis perforans serpiginosa. In eps, there is elimination of altered elastic fibres from papillary layer of dermis to epidermis which is described as transelimination disorder. Elastosis perforans serpiginosa genetic and rare diseases. Elastosis perforans serpiginosa pathology dermnet nz. Jul 01, 2011 rare skin disease in which abnormal elastic tissue fibers, other connective tissue elements and cellular debris are expelled from papillary dermis through epidermis emedicine. Localized perforating serpiginous elastosis in a patient with down syndrome.
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